ophthalmologyОфтальмологияOphthalmology in Russia1816-50952500-0845Ophthalmology10.18008/1816-5095-2019-3-289-295ophthalmology-1005Research ArticleОФТАЛЬМОХИРУРГИЯOPHTHALMOSURGERYХирургическое лечение эпибульбарных пороков развитияSurgical Treatment of Epibulbar MalformationsСаакянС. В.SaakyanS. V.

Саакян Светлана Владимировна - доктор медицинских наук, профессор, начальник отдела офтальмоонкологии и радиологии, зав. учебной частью кафедры глазных болезней ФДПО

Saakyan Svetlana V. - M.D., Ph.D., Prof., head of ocular oncology and radiology department, deputy director of education, ophthalmology faculty

ТацковР. А.TatskovR. A.

Тацков Роберт Александрович - врач отдела офтальмоонкологии и радиологии

Tatskov Robert A. - ohthalmologist of ocular oncology and radiology department

ИвановаО. А.IvanovaO. A.

Иванова Ольга Андреевна - кандидат медицинских наук, врач отдела офтальмоонкологии и радиологии

Ivanova Ol`ga A. - PhD., ohthalmologist of ocular oncology and radiology department

ЦыганковА. Ю.TsygankovA. Yu.

Цыганков Александр Юрьевич - кандидат медицинских наук, младший научный сотрудник отдела офтальмо‑ онкологии и радиологии, ассистент кафедры глазных болезней ФДПО

ул. Садовая-Черногрязская, 14/19, Москва, 105062

ул. Делегатская, 20, стр. 1, Москва, 127473

Tsygankov Alexander I. - PhD, researcher at ocular oncology and radiology department, assistant at ophthalmo‑ logy faculty

Sadovaya-Chernogryazskaya str., 14/19, Moscow, 105062

Delegatskaya str., 20/1, Moscow, 127473

alextsygankov1986@yandex.ruМайбогинА. М.MayboginA. M.

Майбогин Артемий Михайлович - врач отдела патологической анатомии и гистологии

Maybogin Artemii Mikhailovich - ohthalmologist of pathology and histology department

ФГБУ «Московский научно-исследовательский институт глазных болезней им. Гельмгольца» Министерства здравоохранения Российской Федерации; ГБОУ ВПО «Московский государственный медико-стоматологический университет» Министерства здравоохранения Российской ФедерацииРоссияMoscow Helmholtz Research Institute of Eye Diseases; Moscow State Medical Stomatological UniversityRussian FederationФГБУ «Московский научно-исследовательский институт глазных болезней им. Гельмгольца» Министерства здравоохранения Российской ФедерацииРоссияMoscow Helmholtz Research Institute of Eye DiseasesRussian Federation201901102019163289295Copyright © Саакян С.В., Тацков Р.А., Иванова О.А., Цыганков А.Ю., Майбогин А.М., 20192019Саакян С.В., Тацков Р.А., Иванова О.А., Цыганков А.Ю., Майбогин А.М.Saakyan S.V., Tatskov R.A., Ivanova O.A., Tsygankov A.Y., Maybogin A.M.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.ophthalmojournal.com/opht/article/view/1005

Aim. Analysis of the results of surgical treatment in patients with epibulbar malformations. Patients and Methods. The study included 126 patients with a preliminary diagnosis of “epibulbar neoplasm”, who received treatment from January 2013 to December 2017. Male patients were 57.9 % (n = 73), female — 42.1 % (n = 53). The age range was from 6 months to 82 years (13.0 ± 11.4). All patients underwent complex ophthalmological examination and surgical treatment with histological verification of the obtained material. In case of deficiency of own tissues, when the conjunctival defect was closed, plastic was made using an amniotic membrane. Results. 67 (53.2 %) patients had a diagnosis of dermoid of the conjunctiva and / or cornea. In 14.3 % of cases, a diagnosis of lipodermoid with spreading into the eyelids fornix was established. In 7 patients there was a combined lesion, of them in 4 cases with Goldenhar syndrome, 1 case with Jadassohn syndrome and in 2 cases without syndromic disorders. In 10 patients, multicentric lesions were noted with the formation of several dermoids. Choristomas of different structures were identified in 41 patients (32.5 %). Complications of surgical treatment included limitation of eye mobility (n = 9), ptosis of the upper eyelid (n = 7), diplopia (n = 4), ocular deformity (n = 3), corneal perforation (n = 1), symblepharon (n = 1) and entropion (n = 1), which required additional surgical interventions with a favorable functional outcome. Conclusions. Diagnosis of epibulbar malformations requires a comprehensive ophthalmological examination to determine the prevalence of the process, the extent of the lesion in order to plan the timing and tactics of surgical treatment. Congenital epibulbar malformations of the eye are subject to surgical treatment with the growth of lesion, chronic inflammation, cosmetic dissatisfaction and spread to the central parts of the cornea. The use of the amniotic membrane improves normal epithelization and reduces the degree of postoperative scar deformation.

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The authors declare that there are no conflicts of interest present.