ophthalmologyОфтальмологияOphthalmology in Russia1816-50952500-0845Ophthalmology10.18008/1816-5095-2023-2-363-372ophthalmology-2122Research ArticleКЛИНИЧЕСКИЙ СЛУЧАЙCASE REPORTВрожденная аниридия: клинические особенности и терапевтические подходы (клиническое наблюдение)Congenital Aniridia: Clinical Features and Therapeutic Approaches (Case Report)https://orcid.org/0000-0003-4043-456XЮсефН. Ю.YusefN. Yu.

Юсеф Наим Юсеф - доктор медицинских наук, директор, руководитель отдела современных методов лечения в офтальмологии

ул. Россолимо, 11а, б, Москва, 119021, Российская Федерация

Yusef N. Yu. - MD, director, head of the Modern treatment methods in  ophthalmology department

Rossolimo str., 11A, B, Moscow, 119021, Russian Federation

https://orcid.org/0000-0003-1989-6612МакашоваН. В.МakashovaN. V.

Макашова Надежда Васильевна - доктор медицинских наук, старший научный сотрудник отдела глаукомы

ул. Россолимо, 11a, б, 119021, Москва, Российская Федерация

Мakashova Nadezhda V. - MD, senior research officer

Rossolimo str., 11A, B, Moscow, 119021, Russian Federation

nvmakashova@mail.ruhttps://orcid.org/0000-0001-5981-2423ВасилльеваА. Е.VasillyevaA. E.

Василльева Анастасия Евгеньевна - кандидат медицинских наук, руководитель отделения офтальмологии

Ленинский проспект, 90, 119021, Москва, Российская Федерация

Vasillyeva Anastasia E. - РhD, head of the Department of ophthalmology

Leninsky ave., 90, Moscow, 119021, Russian Federation

https://orcid.org/0000-0001-8417-7417АльхумидиК.AlhumidiKh.

Альхумиди Кхалед - кандидат медицинских наук, научный сотрудник отдела современных методовлечения в офтальмологии

ул. Россолимо, 11а, б, Москва, 119021, Российская Федерация

Alhumidi Khaled - РhD, research officer of the Modern treatment methods in ophthalmology department

Rossolimo str., 11A, B, Moscow, 119021, Russian Federation

https://orcid.org/0000-0002-0298-2250РонзинаИ. А.RonzinaI. A.

Ронзина Ирина Адольфовна кандидат медицинских наук, научный сотрудник отдела патологии сетчатки изрительного нерва

ул. Россолимо, 11а, б, Москва, 119021, Российская Федерация

Ronzina Irina A. - PhD, researcher of the Retina and optic nerve pathology department

Rossolimo str., 11A, B, Moscow, 119021, Russian Federation

ФГБНУ «Научно-исследовательский институт глазных болезней им. М.М. Краснова»РоссияM.M. Krasnov Scientific Research Institute of Eye DiseasesRussian FederationООО Медицинский центр «Столица»РоссияMedical Center “Stolitsa”Russian Federation202303072023202363372Copyright © Юсеф Н.Ю., Макашова Н.В., Василльева А.Е., Альхумиди К., Ронзина И.А., 20232023Юсеф Н.Ю., Макашова Н.В., Василльева А.Е., Альхумиди К., Ронзина И.А.Yusef N.Y., Мakashova N.V., Vasillyeva A.E., Alhumidi K., Ronzina I.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.ophthalmojournal.com/opht/article/view/2122

Представлен клинический случай врожденной аниридии в сочетании с гиперметропией высокой степени, врожденной катарактой, офтальмогипертензией, гипоплазией фовеа. В статье проанализированы результаты комплекса морфофункциональных исследований, проведенных до и после хирургического лечения катаракты, представлены практические данные по дифференциальной диагностике глаукомы и офтальмогипертензии, проведен анализ терапевтических подходов, включающий использование диафрагмирующей контактной линзы и трехкомпонентного слезозаместителя Стиллавита.

A clinical case of congenital aniridia in combination with high degree hyperopia, congenital cataract, ophthalmohypertension, foveal hypoplasia is presented. The article analyzes the results of a complex of morphofunctional studies conducted before and after cataract surgery, presents practical data on the differential diagnosis of glaucoma and ophthalmohypertension and analyzes therapeutic approaches, including the use of a diaphragm contact lens and a three-component tear substitute Stillavit.

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The authors declare that there are no conflicts of interest present.